Verbal episodic memory declines prior to diagnosis in Huntington's disease Journal Article uri icon
Overview
abstract
  • Previous studies of verbal episodic memory in pre-diagnostic Huntington's disease (HD) have yielded mixed results; some evidence suggests that memory decline is evident prior to the onset of pronounced neurological signs of HD, whereas other data indicate that memory function remains normal throughout the pre-diagnostic period. This study examines verbal episodic memory in a sample of CAG expanded individuals who have not yet been clinically diagnosed, and who represent a wide range of points along the continuum from health to disease. The Hopkins Verbal Learning Test-Revised (HVLT-R) was administered to 479 participants (428 with the HD CAG expansion and 51 without), and performance was compared to neurobiological indices of disease progression, including a DNA-based estimate of proximity to clinical diagnosis, magnetic resonance imaging (MRI) measures of striatal volume, and neurologist ratings of motor signs. Lower HVLT-R scores were associated with closer proximity to clinical diagnosis and smaller striatal volumes; these relationships were found even in groups with no neurological signs of HD. The CAG expanded groups, including those with only minimal neurological signs, had significantly lower HVLT-R scores than the control group, and performance was worse in sub-groups that had more neurological signs consistent with HD. These findings indicate that verbal episodic memory is affected in early pre-diagnostic HD and may decline as striatal volumes decrease and individuals approach the motor diagnostic threshold.

  • Link to Article
    publication date
  • 2007
  • published in
  • Neuropsychologia  Journal
  • Research
    keywords
  • Age of Onset
  • Confidence Intervals
  • Disease Progression
  • Huntington Disease/*complications/*diagnosis/genetics
  • Memory Disorders/*etiology
  • Neuropsychological Tests
  • Sex Factors
  • Statistics as Topic
  • Verbal Learning/physiology
  • Additional Document Info
    volume
  • 45
  • issue
  • 8